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ICD-10-CM-2023 Diagnosis Codes Overview
ICD-10-CM-2023 > I00-I99 > I26-I28 > I27
I26-I28
Pulmonary heart disease and diseases of pulmonary circulation
I27

Other pulmonary heart diseases

I27.0
Primary pulmonary hypertension
Info:
Heritable pulmonary arterial hypertension
Idiopathic pulmonary arterial hypertension
Primary group 1 pulmonary hypertension
Primary pulmonary arterial hypertension
Excl1.:
persistent pulmonary hypertension of newborn (P29.30)
pulmonary hypertension NOS (I27.20)
secondary pulmonary arterial hypertension (I27.21)
secondary pulmonary hypertension (I27.29)
I27.1
Kyphoscoliotic heart disease
I27.2

Other secondary pulmonary hypertension

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associated underlying condition
Excl1.:
Eisenmenger's syndrome (I27.83)
I27.20
Pulmonary hypertension, unspecified
Info:
Pulmonary hypertension NOS
I27.21
Secondary pulmonary arterial hypertension
Info:
(Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
(Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension
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associated conditions if applicable, or adverse effects of drugs or toxins, such as:
adverse effect of appetite depressants (T50.5X5)
congenital heart disease (Q20-Q28)
human immunodeficiency virus [HIV] disease (B20)
polymyositis (M33.2-)
portal hypertension (K76.6)
rheumatoid arthritis (M05.-)
schistosomiasis (B65.-)
Sjögren syndrome (M35.0-)
systemic sclerosis (M34.-)
I27.22
Pulmonary hypertension due to left heart disease
Info:
Group 2 pulmonary hypertension
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associated left heart disease, if known, such as:
multiple valve disease (I08.-)
rheumatic mitral valve diseases (I05.-)
rheumatic aortic valve diseases (I06.-)
I27.23
Pulmonary hypertension due to lung diseases and hypoxia
Info:
Group 3 pulmonary hypertension
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associated lung disease, if known, such as:
bronchiectasis (J47.-)
cystic fibrosis with pulmonary manifestations (E84.0)
interstitial lung disease (J84.-)
pleural effusion (J90)
sleep apnea (G47.3-)
I27.24
Chronic thromboembolic pulmonary hypertension
Info:
Group 4 pulmonary hypertension
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associated pulmonary embolism, if applicable (I26.-, I27.82)
I27.29
Other secondary pulmonary hypertension
Info:
Group 5 pulmonary hypertension
Pulmonary hypertension with unclear multifactorial mechanisms
Pulmonary hypertension due to hematologic disorders
Pulmonary hypertension due to metabolic disorders
Pulmonary hypertension due to other systemic disorders
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other associated disorders, if known, such as:
chronic myeloid leukemia (C92.10-C92.22)
essential thrombocythemia (D47.3)
Gaucher disease (E75.22)
hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
hyperthyroidism (E05.-)
hypothyroidism (E00-E03)
polycythemia vera (D45)
sarcoidosis (D86.-)
I27.8

Other specified pulmonary heart diseases

I27.81
Cor pulmonale (chronic)
Info:
Cor pulmonale NOS
Excl1.:
acute cor pulmonale (I26.0-)
I27.82
Chronic pulmonary embolism
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code, if applicable, for associated long-term (current) use of anticoagulants (Z79.01)
Excl1.:
personal history of pulmonary embolism (Z86.711)
I27.83
Eisenmenger's syndrome
Info:
Eisenmenger's complex
(Irreversible) Eisenmenger's disease
Pulmonary hypertension with right to left shunt related to congenital heart disease
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underlying heart defect, if known, such as:
atrial septal defect (Q21.1-)
Eisenmenger's defect (Q21.8)
patent ductus arteriosus (Q25.0)
ventricular septal defect (Q21.0)
I27.89
Other specified pulmonary heart diseases
I27.9
Pulmonary heart disease, unspecified
Info:
Chronic cardiopulmonary disease

 

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