ICD   PCS   Disclaimer
ICD-10-CM-2017 Diagnosis Codes Overview
ICD-10-CM-2017 > E00-E89 > E70-E88 > E88
E70-E88
Metabolic disorders
Excl1.:
androgen insensitivity syndrome (icd E34.5 Androgen insensitivity syndromeE34.5-)
congenital adrenal hyperplasia (icd E25.0 Congenital adrenogenital disorders associated with enzyme deficiencyE25.0)
Ehlers-Danlos syndrome (icd Q79.6 Ehlers-Danlos syndromeQ79.6)
hemolytic anemias attributable to enzyme disorders (icd D55 Anemia due to enzyme disordersD55.-)
Marfan's syndrome (icd Q87.4 Marfan's syndromeQ87.4)
5-alpha-reductase deficiency (icd E29.1 Testicular hypofunctionE29.1)
E88

Other and unspecified metabolic disorders

Use add'l
codes for associated conditions
Excl1.:
histiocytosis X (chronic) (icd C96.6 Unifocal Langerhans-cell histiocytosisC96.6)
E88.0

Disorders of plasma-protein metabolism, not elsewhere classified

Excl1.:
disorder of lipoprotein metabolism (icd E78 Disorders of lipoprotein metabolism and other lipidemiasE78.-)
monoclonal gammopathy (of undetermined significance) (icd D47.2 Monoclonal gammopathyD47.2)
polyclonal hypergammaglobulinemia (icd D89.0 Polyclonal hypergammaglobulinemiaD89.0)
Waldenström macroglobulinemia (icd C88.0 Waldenström macroglobulinemiaC88.0)
E88.01
Alpha-1-antitrypsin deficiency
Info:
AAT deficiency
E88.09
Other disorders of plasma-protein metabolism, not elsewhere classified
Info:
Bisalbuminemia
E88.1
Lipodystrophy, not elsewhere classified
Info:
Lipodystrophy NOS
Excl1.:
Whipple's disease (icd K90.81 Whipple's diseaseK90.81)
E88.2
Lipomatosis, not elsewhere classified
Info:
Lipomatosis NOS
Lipomatosis (Check) dolorosa [Dercum]
E88.3
Tumor lysis syndrome
Info:
Tumor lysis syndrome (spontaneous)
Tumor lysis syndrome following antineoplastic drug chemotherapy
Use add'l
code for adverse effect, if applicable, to identify drug (icd T45.1X5 Adverse effect of antineoplastic and immunosuppressive drugsT45.1X5)
E88.4

Mitochondrial metabolism disorders

Excl1.:
disorders of pyruvate metabolism (icd E74.4 Disorders of pyruvate metabolism and gluconeogenesisE74.4)
Kearns-Sayre syndrome (icd H49.81 Kearns-Sayre syndromeH49.81)
Leber's disease (icd H47.22 Hereditary optic atrophyH47.22)
Leigh's encephalopathy (icd G31.82 Leigh's diseaseG31.82)
Mitochondrial myopathy, NEC (icd G71.3 Mitochondrial myopathy, not elsewhere classifiedG71.3)
Reye's syndrome (icd G93.7 Reye's syndromeG93.7)
E88.40
Mitochondrial metabolism disorder, unspecified
E88.41
MELAS syndrome
Info:
Mitochondrial myopathy, encephalopathy, lactic acidosis and stroke-like episodes
E88.42
MERRF syndrome
Info:
Myoclonic epilepsy associated with ragged-red fibers
Use add'l
progressive myoclonic epilepsy (icd G40.3 Generalized idiopathic epilepsy and epileptic syndromesG40.3-)
E88.49
Other mitochondrial metabolism disorders
E88.8

Other specified metabolic disorders

E88.81
Metabolic syndrome
Info:
Dysmetabolic syndrome X
Use add'l
codes for associated manifestations, such as:
obesity (icd E66 Overweight and obesityE66.-)
E88.89
Other specified metabolic disorders
Info:
Launois-Bensaude adenolipomatosis
Excl1.:
adult pulmonary Langerhans cell histiocytosis (icd J84.82 Adult pulmonary Langerhans cell histiocytosisJ84.82)
E88.9
Metabolic disorder, unspecified


ICD-10-CM-2017 Code Search Engine and PCS-2017 Code Search Engine