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ICD-10-CM-2017 Diagnosis Codes Overview
ICD-10-CM-2017 > D50-D89 > D80-D89 > D89
D80-D89
Certain disorders involving the immune mechanism
Incl.:
defects in the complement system
immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
sarcoidosis
Excl1.:
autoimmune disease (systemic) NOS (icd M35.9 Systemic involvement of connective tissue, unspecifiedM35.9)
functional disorders of polymorphonuclear neutrophils (icd D71 Functional disorders of polymorphonuclear neutrophilsD71)
human immunodeficiency virus [HIV] disease (icd B20 Human immunodeficiency virus [HIV] diseaseB20)
D89

Other disorders involving the immune mechanism, not elsewhere classified

Excl1.:
hyperglobulinemia NOS (icd R77.1 Abnormality of globulinR77.1)
monoclonal gammopathy (of undetermined significance) (icd D47.2 Monoclonal gammopathyD47.2)
Excl2.:
transplant failure and rejection (icd T86 Complications of transplanted organs and tissueT86.-)
D89.0
Polyclonal hypergammaglobulinemia
Info:
Benign hypergammaglobulinemic purpura
Polyclonal gammopathy NOS
D89.1
Cryoglobulinemia
Info:
Cryoglobulinemic purpura
Cryoglobulinemic vasculitis
Essential cryoglobulinemia
Idiopathic cryoglobulinemia
Mixed cryoglobulinemia
Primary cryoglobulinemia
Secondary cryoglobulinemia
D89.2
Hypergammaglobulinemia, unspecified
D89.3
Immune reconstitution syndrome
Info:
Immune reconstitution inflammatory syndrome [IRIS]
Use add'l
code for adverse effect, if applicable, to identify drug (icd T36-T50 Poisoning by, adverse effects of and underdosing of drugs, medicaments and biological substances T36-T50 with fifth or sixth character 5)
D89.4

Mast cell activation syndrome and related disorders

Excl1.:
aggressive systemic mastocytosis (icd C96.2 Malignant mast cell tumorC96.2)
cutaneous mastocytosis (icd Q82.2 MastocytosisQ82.2)
indolent systemic mastocytosis (icd D47.0 Histiocytic and mast cell tumors of uncertain behaviorD47.0)
malignant mastocytoma (icd C96.2 Malignant mast cell tumorC96.2)
mast cell leukemia (icd C94.3 Mast cell leukemiaC94.3-)
mastocytoma (icd D47.0 Histiocytic and mast cell tumors of uncertain behaviorD47.0)
systemic mastocytosis associated with a clonal hematologic non-mast cell lineage disease (SM-AHNMD) (icd D47.0 Histiocytic and mast cell tumors of uncertain behaviorD47.0)
D89.40
Mast cell activation, unspecified
Info:
Mast cell activation disorder, unspecified
Mast cell activation syndrome, NOS
D89.41
Monoclonal mast cell activation syndrome
D89.42
Idiopathic mast cell activation syndrome
D89.43
Secondary mast cell activation
Info:
Secondary mast cell activation syndrome
Use add'l
underlying etiology, if known
D89.49
Other mast cell activation disorder
Info:
Other mast cell activation syndrome
D89.8

Other specified disorders involving the immune mechanism, not elsewhere classified

D89.81
Graft-versus-host disease
Code first
underlying cause, such as:
complications of transplanted organs and tissue (icd T86 Complications of transplanted organs and tissueT86.-)
complications of blood transfusion (icd T80.89 Other complications following infusion, transfusion and therapeutic injectionT80.89)
Use add'l
code to identify associated manifestations, such as:
desquamative dermatitis (icd L30.8 Other specified dermatitisL30.8)
diarrhea (icd R19.7 Diarrhea, unspecifiedR19.7)
elevated bilirubin (icd R17 Unspecified jaundiceR17)
hair loss (icd L65.9 Nonscarring hair loss, unspecifiedL65.9)
D89.810
Acute graft-versus-host disease
D89.811
Chronic graft-versus-host disease
D89.812
Acute on chronic graft-versus-host disease
D89.813
Graft-versus-host disease, unspecified
D89.82
Autoimmune lymphoproliferative syndrome [ALPS]
D89.89
Other specified disorders involving the immune mechanism, not elsewhere classified
Excl1.:
human immunodeficiency virus disease (icd B20 Human immunodeficiency virus [HIV] diseaseB20)
D89.9
Disorder involving the immune mechanism, unspecified
Info:
Immune disease NOS


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