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ICD-10-CM-2023 Diagnosis Codes Overview
ICD-10-CM-2023 > D50-D89 > D80-D89 > D81
D80-D89
Certain disorders involving the immune mechanism
Incl.:
defects in the complement system
immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
sarcoidosis
Excl1.:
autoimmune disease (systemic) NOS (M35.9)
functional disorders of polymorphonuclear neutrophils (D71)
human immunodeficiency virus [HIV] disease (B20)
D81

Combined immunodeficiencies

Excl1.:
autosomal recessive agammaglobulinemia (Swiss type) (D80.0)
D81.0
Severe combined immunodeficiency [SCID] with reticular dysgenesis
D81.1
Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
D81.2
Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
D81.3

Adenosine deaminase [ADA] deficiency

D81.30
Adenosine deaminase deficiency, unspecified
Info:
ADA deficiency NOS
D81.31
Severe combined immunodeficiency due to adenosine deaminase deficiency
Info:
ADA deficiency with SCID
Adenosine deaminase [ADA] deficiency with severe combined immunodeficiency
D81.32
Adenosine deaminase 2 deficiency
Info:
ADA2 deficiency
Adenosine deaminase deficiency type 2
Use add'l
, if applicable, any associated manifestations, such as:
polyarteritis nodosa (M30.0)
stroke (I63.-)
D81.39
Other adenosine deaminase deficiency
Info:
Adenosine deaminase [ADA] deficiency type 1, NOS
Adenosine deaminase [ADA] deficiency type 1, without SCID
Adenosine deaminase [ADA] deficiency type 1, without severe combined immunodeficiency
Partial ADA deficiency (type 1)
Partial adenosine deaminase deficiency (type 1)
D81.4
Nezelof's syndrome
D81.5
Purine nucleoside phosphorylase [PNP] deficiency
D81.6
Major histocompatibility complex class I deficiency
Info:
Bare lymphocyte syndrome
D81.7
Major histocompatibility complex class II deficiency
D81.8

Other combined immunodeficiencies

D81.81
Biotin-dependent carboxylase deficiency
Info:
Multiple carboxylase deficiency
Excl1.:
biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)
D81.810
Biotinidase deficiency
D81.818
Other biotin-dependent carboxylase deficiency
Info:
Holocarboxylase synthetase deficiency
Other multiple carboxylase deficiency
D81.819
Biotin-dependent carboxylase deficiency, unspecified
Info:
Multiple carboxylase deficiency, unspecified
D81.82
Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]
Info:
p110d-activating mutation causing senescent T cells, lymphadenopathy, and immunodeficiency [PASLI] disease
Use add'l
, if applicable, any associated manifestations, such as:
bronchiectasis (J47.-)
herpes virus infections (B00.-)
other acute respiratory tract infections (J00-J06; J20-J22)
other infections (A00-B99)
pneumonia (J12-J18)
D81.89
Other combined immunodeficiencies
D81.9
Combined immunodeficiency, unspecified
Info:
Severe combined immunodeficiency disorder [SCID] NOS

 

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