ICD-10-CM-2023 > D50-D89 > D80-D89 > D81 |
D80-D89 | Certain disorders involving the immune mechanism | |
Incl.: | defects in the complement system immunodeficiency disorders, except human immunodeficiency virus [HIV] disease sarcoidosis | |
Excl1.: | autoimmune disease (systemic) NOS (M35.9) functional disorders of polymorphonuclear neutrophils (D71) human immunodeficiency virus [HIV] disease (B20) | |
D81 | Combined immunodeficiencies | |
Excl1.: | autosomal recessive agammaglobulinemia (Swiss type) (D80.0) | |
D81.0 | Severe combined immunodeficiency [SCID] with reticular dysgenesis | |
D81.1 | Severe combined immunodeficiency [SCID] with low T- and B-cell numbers | |
D81.2 | Severe combined immunodeficiency [SCID] with low or normal B-cell numbers | |
D81.3 | Adenosine deaminase [ADA] deficiency | |
D81.30 | Adenosine deaminase deficiency, unspecified | |
Info: | ADA deficiency NOS | |
D81.31 | Severe combined immunodeficiency due to adenosine deaminase deficiency | |
Info: | ADA deficiency with SCID Adenosine deaminase [ADA] deficiency with severe combined immunodeficiency | |
D81.32 | Adenosine deaminase 2 deficiency | |
Info: | ADA2 deficiency Adenosine deaminase deficiency type 2 | |
Use add'l | , if applicable, any associated manifestations, such as: polyarteritis nodosa (M30.0) stroke (I63.-) | |
D81.39 | Other adenosine deaminase deficiency | |
Info: | Adenosine deaminase [ADA] deficiency type 1, NOS Adenosine deaminase [ADA] deficiency type 1, without SCID Adenosine deaminase [ADA] deficiency type 1, without severe combined immunodeficiency Partial ADA deficiency (type 1) Partial adenosine deaminase deficiency (type 1) | |
D81.4 | Nezelof's syndrome | |
D81.5 | Purine nucleoside phosphorylase [PNP] deficiency | |
D81.6 | Major histocompatibility complex class I deficiency | |
Info: | Bare lymphocyte syndrome | |
D81.7 | Major histocompatibility complex class II deficiency | |
D81.8 | Other combined immunodeficiencies | |
D81.81 | Biotin-dependent carboxylase deficiency | |
Info: | Multiple carboxylase deficiency | |
Excl1.: | biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8) | |
D81.810 | Biotinidase deficiency | |
D81.818 | Other biotin-dependent carboxylase deficiency | |
Info: | Holocarboxylase synthetase deficiency Other multiple carboxylase deficiency | |
D81.819 | Biotin-dependent carboxylase deficiency, unspecified | |
Info: | Multiple carboxylase deficiency, unspecified | |
D81.82 | Activated Phosphoinositide 3-kinase Delta Syndrome [APDS] | |
Info: | p110d-activating mutation causing senescent T cells, lymphadenopathy, and immunodeficiency [PASLI] disease | |
Use add'l | , if applicable, any associated manifestations, such as: bronchiectasis (J47.-) herpes virus infections (B00.-) other acute respiratory tract infections (J00-J06; J20-J22) other infections (A00-B99) pneumonia (J12-J18) | |
D81.89 | Other combined immunodeficiencies | |
D81.9 | Combined immunodeficiency, unspecified | |
Info: | Severe combined immunodeficiency disorder [SCID] NOS |
ICD-10-CM-2023 Code Search Engine and PCS-2023 Code Search Engine |