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ICD-10-CM-2017 Diagnosis Codes Overview
ICD-10-CM-2017 > E00-E89 > E70-E88 > E76
E70-E88
Metabolic disorders
Excl1.:
androgen insensitivity syndrome (icd E34.5 Androgen insensitivity syndromeE34.5-)
congenital adrenal hyperplasia (icd E25.0 Congenital adrenogenital disorders associated with enzyme deficiencyE25.0)
Ehlers-Danlos syndrome (icd Q79.6 Ehlers-Danlos syndromeQ79.6)
hemolytic anemias attributable to enzyme disorders (icd D55 Anemia due to enzyme disordersD55.-)
Marfan's syndrome (icd Q87.4 Marfan's syndromeQ87.4)
5-alpha-reductase deficiency (icd E29.1 Testicular hypofunctionE29.1)
E76

Disorders of glycosaminoglycan metabolism

E76.0

Mucopolysaccharidosis, type I

E76.01
Hurler's syndrome
E76.02
Hurler-Scheie syndrome
E76.03
Scheie's syndrome
E76.1
Mucopolysaccharidosis, type II
Info:
Hunter's syndrome
E76.2

Other mucopolysaccharidoses

E76.21
Morquio mucopolysaccharidoses
E76.210
Morquio A mucopolysaccharidoses
Info:
Classic Morquio syndrome
Morquio syndrome A
Mucopolysaccharidosis, type IVA
E76.211
Morquio B mucopolysaccharidoses
Info:
Morquio-like mucopolysaccharidoses
Morquio-like syndrome
Morquio syndrome B
Mucopolysaccharidosis, type IVB
E76.219
Morquio mucopolysaccharidoses, unspecified
Info:
Morquio syndrome
Mucopolysaccharidosis, type IV
E76.22
Sanfilippo mucopolysaccharidoses
Info:
Mucopolysaccharidosis, type III (A) (B) (C) (D)
Sanfilippo A syndrome
Sanfilippo B syndrome
Sanfilippo C syndrome
Sanfilippo D syndrome
E76.29
Other mucopolysaccharidoses
Info:
beta-Glucuronidase deficiency
Maroteaux-Lamy (mild) (severe) syndrome
Mucopolysaccharidosis, types VI, VII
E76.3
Mucopolysaccharidosis, unspecified
E76.8
Other disorders of glucosaminoglycan metabolism
E76.9
Glucosaminoglycan metabolism disorder, unspecified


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