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ICD-10-CM-2023 Diagnosis Codes Overview
ICD-10-CM-2023 > E00-E89 > E70-E88 > E75
E70-E88
Metabolic disorders
Excl1.:
androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan's syndrome (Q87.4)
5-alpha-reductase deficiency (E29.1)
Excl2.:
Ehlers-Danlos syndromes (Q79.6-)
E75

Disorders of sphingolipid metabolism and other lipid storage disorders

Excl1.:
mucolipidosis, types I-III (E77.0-E77.1)
Refsum's disease (G60.1)
E75.0

GM2 gangliosidosis

E75.00
GM2 gangliosidosis, unspecified
E75.01
Sandhoff disease
E75.02
Tay-Sachs disease
E75.09
Other GM2 gangliosidosis
Info:
Adult GM2 gangliosidosis
Juvenile GM2 gangliosidosis
E75.1

Other and unspecified gangliosidosis

E75.10
Unspecified gangliosidosis
Info:
Gangliosidosis NOS
E75.11
Mucolipidosis IV
E75.19
Other gangliosidosis
Info:
GM1 gangliosidosis
GM3 gangliosidosis
E75.2

Other sphingolipidosis

Excl1.:
adrenoleukodystrophy [Addison-Schilder] (E71.528)
E75.21
Fabry (-Anderson) disease
E75.22
Gaucher disease
E75.23
Krabbe disease
E75.24
Niemann-Pick disease
Info:
Acid sphingomyelinase deficiency (ASMD)
E75.240
Niemann-Pick disease type A
Info:
Acid sphingomyelinase deficiency type A (ASMD type A)
Infantile neurovisceral acid sphingomyelinase deficiency
E75.241
Niemann-Pick disease type B
Info:
Acid sphingomyelinase deficiency type B (ASMD type B)
Chronic visceral acid sphingomyelinase deficiency
E75.242
Niemann-Pick disease type C
E75.243
Niemann-Pick disease type D
E75.244
Niemann-Pick disease type A/B
Info:
Acid sphingomyelinase deficiency type A/B (ASMD type A/B)
Chronic neurovisceral acid sphingomyelinase deficiency
E75.248
Other Niemann-Pick disease
E75.249
Niemann-Pick disease, unspecified
Info:
Acid sphingomyelinase deficiency (ASMD) NOS
E75.25
Metachromatic leukodystrophy
E75.26
Sulfatase deficiency
Info:
Multiple sulfatase deficiency (MSD)
E75.29
Other sphingolipidosis
Info:
Farber's syndrome
Sulfatide lipidosis
E75.3
Sphingolipidosis, unspecified
E75.4
Neuronal ceroid lipofuscinosis
Info:
Batten disease
Bielschowsky-Jansky disease
Kufs disease
Spielmeyer-Vogt disease
E75.5
Other lipid storage disorders
Info:
Cerebrotendinous cholesterosis [van Bogaert-Scherer-Epstein]
Wolman's disease
E75.6
Lipid storage disorder, unspecified

 

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